Surgical Management of Tympanojugulare Paragangliomas: A Rare and Challenging Case of Vascular Neoplasma

DOI

10.2991/ahsr.k.220206.044How to use a DOI?

Keywords

Paragangliomas; Tympanojugular

Abstract

Tympanojugulare paragangliomas (TJPs) are benign tumors arising from neural crest cells located along the jugular bulbus and the tympanic plexus. TJPs have always presented a challenge to surgeons due to the fact that these tumors are vascularize and locally aggressive and involve important neurovascular structures. The treatment is guided by the classification of Fisch. We present a case of 54 years woman with a mass in the right ear canal associated with pulsatile tinnitus, hearing impairment and multiple lower cranial nerves palsy (CN VII, Xl & Xll). The clinical manifestations and paraclinical investigations established the diagnosis of tympanojugulare paraganglioma Fisch B2. According to the preoperative plan of the case, we decided to resected the tumour subtotally with canal wall down mastoidectomy procedure. Postoperative evaluation shows good healing and improvement of all the symptoms. The evidence-based literature search regarding the management of TJP using ‘tympanojugulare paraganglioma as keynwords was conducted on PubMed. Further selection is based on inclusion and exclusion criterion. four journals obtained are case reports and related to our case based on clinical manifestation and management of TJPs. The jugulotympanic paraganglioma have the tendency to involve multiple vital structures of the skull base. In most of these tumors, surgery remains the mainstay treatment. A detailed preoperative plan of treatment is required to maximize tumor resection, minimizing morbidity of the great vessels and lower cranial nerves and optimize the result.

Copyright

© 2022 The Authors. Published by Atlantis Press International B.V.

Open Access

This is an open access article under the CC BY-NC license.

Download article (PDF)

TY  - CONF
AU  - Dinna Astrib
AU  - Masyita Gaffar
AU  - Nova Pieter
PY  - 2022
DA  - 2022/02/21
TI  - Surgical Management of Tympanojugulare Paragangliomas: A Rare and Challenging Case of Vascular Neoplasma
BT  - Proceedings of the 2nd Global Health and Innovation in conjunction with 6th ORL Head and Neck Oncology Conference (ORLHN 2021)
PB  - Atlantis Press
SP  - 231
EP  - 241
SN  - 2468-5739
UR  - https://doi.org/10.2991/ahsr.k.220206.044
DO  - 10.2991/ahsr.k.220206.044
ID  - Astrib2022
ER  -